小儿直肠重复畸形（附7例报告）

报告经病理及手术证实的直肠重复畸形７例，其中３例为囊肿型，４例为管状直肠重复畸形。囊肿型的主要症状为瘘口经久不愈及肿物压迫造成的排便困难。管状直肠重复畸形的主要症状为排便困难，并伴有不同形式的泌尿生殖系统畸形。７例患儿中４例伴有脊柱畸形。     

重复肾,重复输尿管畸形的诊断与治疗（附20例报告）

报告重复肾，重复输尿管畸形２０例，其中单侧畸形１５例，双侧畸形５例，并发输尿管异位开口８例，输尿管囊肿４例，重复肾上肾积水７例，重复肾上肾发育不良伴下肾积水，输尿管末端狭窄１例，结合文献分析了ＩＶＵ，Ｂ超和ＣＴ的诊断价值，提出了ＣＴ对双侧重复畸形伴一侧输尿管异位开口具有定侧诊断价值，指出可针对不同情况采取相应的治疗方法及手术方式。     

小儿胃重复畸形4例报告

胃重复畸形患病率低,在胃肠道重复畸形中不足9％[1].发病机制仍不清楚,可能与原始前肠空泡化异常、脊索分离、成管发育缺陷等相关[2].胃重复畸形可分为囊肿型和管状型,其中不与消化道相通的囊肿型最为常见.虽然超声、CT、胃镜、消化道造影均可用于早期诊断,但病理仍为诊断金标准.胃重复畸形为良性病变,但随着病变发展,会导致炎...     

全结肠、直肠重复畸形四例诊治经验

目的提高对全结肠、直肠重复畸形的认识，减少误诊。方法对4例全结肠、直肠重复畸形的诊治进行总结。结果3例重复肠管开口在舟状窝，1例重复肠管远端为盲端。4例中2例合并泌尿生殖畸形，其中1例同时合并先天性肛门闭锁，其重复肠管与主肠管分别开口在舟状窝处，术前误诊。3例行主肠管与重复肠管的开窗术，1例行全结肠切除术。4例术后均恢复良好。结论全结肠、直肠重复畸形常合并有泌尿、生殖系统畸形，钡灌肠X线检查可确诊。治疗可采用全结肠切除、重复肠管黏膜剥脱及重复肠管与主肠管开窗术。     

真两性畸形的诊断与治疗(附11例报告)

真两性畸形系指体内同时存在卵巢和睾丸两种性腺组织的一类疾病，在性别畸形中约占２０％。我院１９７８～１９９７年共收治１１例，报告如下。临床资料　本组１１例。社会性别女７例，男４例。就诊年龄４～２８岁，平均１６岁。临床表现为外生殖器畸形，抚养为男性者有青春期乳房发育２例，周期性腹痛２例及腹股沟包块２例；抚养为女性者有闭经４例、周期性腹痛２例及腹股沟包块３例。性腺按Ｈｉｎｍａｎ法分类，双侧型２例，分侧型３例，单侧型６例。１１例２２个性腺中，卵睾１０个，卵巢７个，睾丸５个。７个卵巢均有输卵管，１０个卵睾…     

输尿管囊肿脱出1例报告

异位输尿管囊肿脱出于尿道口外多见于女性，常合并重复肾双输尿管畸形，临床表现为尿道外口红色囊性肿块，挤压后可还纳、消失，伴有排尿困难、疼痛、出血和腰部胀痛等症状。成人输尿管囊肿脱出临床罕见，我们收治成人单一肾输尿管囊肿脱出1例，现报告如下。     

肾、输尿管、膀胱及尿道重复畸形一例报告

肾、输尿管、膀胱及尿道重复畸形一例报告孙棠山，高银刚，陈树波，魏俊利肾、输尿管、膀胱及尿道全泌尿系统重复畸形临床罕见，我院收治１例。报告如下。患儿，女，２岁。因排尿困难，用力排尿时尿道内脱出一肿物６个月余，于１９９４年７月１２日入院。患儿入院前４个月...     

贲门癌术后食管重复癌2例报告

贲门癌术后食管重复癌２例报告北京医科大学人民医院（１０００４４）李萝赞，张国良我院收治贲门癌术后食管重复癌２例，报道如下。例１．男性，４４岁。７年前曾行责门癌根治、食管胃主动脉弓下吻合术。病理结果：贲门部管状腺癌４ｃｍ×４ｃｍ，上下断端（一），肿瘤周...     

网管状镍钛合金支架治疗直肠梗阻10例

我院自１９９５年１０月至１９９８年９月用自行设计的网管状镍钛形状记忆合金支架治疗结直肠梗阻１０例。一、材料与方法本组男７例，女３例，年龄２９～８０岁，平均５５岁。急性梗阻３例，慢性梗阻７例。通过腹平片、直肠或乙状结肠镜检查及活检明确诊断。病灶位于直肠...     

小儿重复肾合并其他尿路畸形（附60例报告）

６０例重复肾中，４８例合并输尿管口异位，７例合并输尿管囊肿，４例伴巨大输尿管积水，５例合并肾发育不良，１例为肾积水。年龄４个月～１３岁。临床表现：滴沥性尿失禁４８例，尿路感染１０例，腹部包块６例，排尿困难５例，尿道口有肿物脱出４例。诊断主要依靠ＩＶＵ。５８例经手术治疗，其中５１例作患侧上肾部及输尿管切除，７例行患侧肾切除。术后除１例尿内仍有异常外，均恢复满意。     

Duplications of the lower urinary tract in children

Seven cases of bladder duplication are described, and compared with 27 cases of urethral duplication. Bladder duplication was collateral while urethral duplication was usually in the sagittal plane. The conditions may coexist when the duplication of the bladder extends caudally to produce a collateral urethral duplication, but in one boy bladder duplication was associated with 4 urethrae in the sagittal plane. In 5 cases the bladders were united; in 2 cases, one bladder was excised. The results were satisfactory in 6 and in one the bladder failed to empty. The basic defects that lead to duplication are unknown. Several features of the conditons suggest that there are different aetiologies in each type. There are similarities with the exstrophy epispadias complex. Even when there are major abnormalities in other systems the general and urological prognosis is good.     

女性输尿管完全重复畸形的诊治(附38例报告)

目的探讨女性输尿管完全重复畸形的诊断及治疗。方法回顾性分析2000年1月至2005年12月所收治并获得随访的38例女性输尿管完全重复畸形患者。影像学检查确定诊断,所有患者均进行手术治疗。结果术后取得满意疗效,无进行性肾积水、肾功能损害,尿失禁完全消失。结论影像学检查在女性输尿管完全重复畸形的诊断中意义重大,手术治疗可取得满意疗效。     

Duplicated urethra: an anomaly best repaired

Three cases of urethral duplication are described—two complete and one incomplete. The surgical approaches used in 2 of the 3 cases are described, the third not having come to definitive surgery as yet. In the patient with an incomplete urethral duplication the accessory urethra and associated ventral preputial hood were excised. A repair of the complete duplication was devised in which an end-to-side urethrourethrostomy and penile plastic revision were accomplished. The literature is reviewed and a new classification system for urethral duplication is proposed.     

Duodenal duplication. Report of 2 cases in adults and review of the literature

Two cases of adult male patients with symptomatic duodenal duplication cysts are reported. The clinical manifestations were vomiting and epigastric pain in the first case and recurrent pancreatitis with a palpable mass in the right upper quadrant of the abdomen in the second. In both cases the diagnosis was only histological and the patients recovered after local excision of the duplication and duodenopancreatectomy, respectively. These two cases prompted an evaluation of the diagnostic features and surgical treatment of duodenal duplication cysts.     

重复输尿管21例报告

目的 提高重复输尿管异常的诊治效果。方法 总结21例重复输尿管患者的临床资料，其中完全性单侧重复输尿管14例，不完全性单侧重复输尿管4例，完全性双侧重复输尿管3例。结果 完全性单侧者切除病变半肾及输尿管10例，膀胱输尿管吻合4例。不完全性单侧者4例行输尿管侧侧吻合。完全性双侧者切除病变较重侧上半肾输尿管2例，行同侧输尿管膀胱吻合1例。术后6个月，3例双侧者尿路感染症状减轻，18例单侧者无尿路感染及返流症状。非半肾切除9例随访12-36个月，仅1例膀胱输尿管吻合者因脓肾行吻合侧肾切除。结论 重复输尿管异常应重视影像学检查，术前正确评估上半肾功能，术后应长期随访。     

三维CT尿路成像对小儿重复肾输尿管畸形的诊断价值

目的　寻求诊断小儿重复肾输尿管畸形的最佳检查方法 ,比较三维CT尿路成像(CTU)与IVU、磁共振尿路成像 (MRU)诊断重复肾输尿管畸形的价值。　方法　 18例疑重复肾输尿管畸形患儿行CTU检查 ,其中 11例曾行IVU检查 ,4例曾行MRU检查。　结果　CTU诊断重复肾输尿管 18例 ,合并重复输尿管下端囊肿 8例 ,重复输尿管异位开口 10例 ,全部经手术证实。11例IVU检查者明确诊断 3例 ,4例行MRU检查者明确诊断 1例。　结论　CTU能为诊断重复肾输尿管畸形提供确切依据     

Enteric and rectal duplications and duplication cysts in the adult

Alimentary tract duplication and duplication cysts are rare congenital malformations. The ileum is the most frequently affected site. However, alimentary tract duplication and duplication cysts can occur at any point along the gastrointestinal tract. Early diagnosis and prompt surgical treatment is the best way to prevent associated morbidity. This article presents the cases of three patients admitted to Gulhane Military Medical Academy with signs of acute abdomen, intra-abdominal mass and chronic abdominal pain. These patients were found to have enteric duplication, duplication cyst and/or retro-rectal cyst. The literature on alimentary tract duplications is reviewed.     

Gastric duplication.

Vomiting and failure to thrive were the presenting complaints of a patient with gastric duplication. The case is presented and features of gastric duplication are summarized with other cases reported in the literature.     

Duplication of the intestinal tract

Twelve duplications of the alimentary tract in eleven children are reviewed. There was a predominance of the spheric type of duplication as well as the neonatal group of children with clinical sign of tumour in most cases. There were no major problems in resection of spheric duplications but tubular type cases afforded different procedure in each case. Three cases with associated atresias were noted. There was one death related to gastric duplication.     

Urethral duplication in boys: report of 4 cases

Urethral duplication is a rare anomaly, affecting mainly boys. The clinical presentation varies because of the different anatomical patterns of this abnormality. We report 4 cases of urethral duplication in children. An epispadiac duplication was present in 1 case, hypospadiac duplication in 1 case, Y-duplication in 1 case and a congenital prepubic sinus in the last case. The pre-operative probe was based on urethrocystography and fistulography. The surgical management included excision of the duplicated urethra in 3 cases. Transurethral incision of the intra-urethral septum was performed in the case of hypospadiac duplication. The characteristics of male urethral duplication are reviewed.