Biliary atresia associated with multiple unrelated anomalies: what about it?

The prognosis of extrahepatic biliary atresia (EHBA) and multiple apparently not linked anomalies has never been disclosed. We reported a rare case affected by biliary, anorectal and esophageal atresia, and collected the uncommon associations of EHBA with multiple unrelated congenital defects to make known the prognosis. An elevated rate of hepatic failure despite surgery and an early poor outcome were found in the above-mentioned associations. A liver transplantation at the first months of life could be considered to improve outcome.     

中重度阻塞性睡眠呼吸暂停低通气综合征围手术期治疗

目的探讨中重度阻塞性睡眠呼吸暂停低通气综合征（obstructive sleep apnea hypopnea syndrome,OSAHS）的围手术期治疗。方法回顾分析42例中重度OSAHS患者围手术期处理临床资料,包括术前全身病情评估与处理,术前术后经鼻持续正压通气（continuous positive airway pressure,CPAP）治疗,麻醉风险评估与处理,麻醉术后恢复期处理,术后重症监护中心（intensive care unit,ICU）处理。结果围手术期无呼吸道梗阻发生,术后6个月疗效总有效率92．86％。结论中重度OSAHS患者围手术期危险性高,认真进行围手术期处理,可以降低手术风险,防止重大并发症发生。     

阻塞性睡眠呼吸暂停低通气综合征患者亚临床右心室功能障碍的肺动脉硬化度

目的:研究阻塞性睡眠呼吸暂停低通气综合征(OSAHS)患者发生亚临床的右心室功能障碍时其肺动脉硬化度(PAS)的变化.方法:实验组选取的是经多导睡眠监测仪(PSG)确诊的80例OSAHS患者,根据AHI的不同分成3组,对照组选取的是同一时间段的35例健康者.使用二维超声收集所需常规超声参数,使用速度向量成像(VVI)技...     

睡眠呼吸障碍儿童总脑电醒觉反应指数的临床研究

目的 探讨影响睡眠呼吸障碍(sleep disordered breathing,SDB)患儿总脑电醒觉反应指数(arousal index,ArI)的因素.方法 2018年3月～2019年3月因疑似阻塞性睡眠呼吸暂停低通气综合征(OSAHS)而进行多道睡眠监测的75例患儿作为研究对象,OSAHS的诊断标准采用《儿童阻...     

基于《血证论》治血四法探讨过敏性紫癜的中医证治

过敏性紫癜的主要病机为热、瘀、虚,治疗以清热凉血、活血消瘀、养阴宁络、健脾补虚为治则,清热止血为第一要法,活血消瘀以防复发,养阴宁络以防血复动,健脾益气摄血以善后收功,且活血消瘀贯穿整个治疗过程.过敏性紫癜的中医证治充分验证了唐容川的止血四法:止血,消瘀,宁血,补虚,临证治疗具有显著疗效,故治血四法对过敏性紫癜的治疗具...     

《血证论》血下泄证论治规律研究

运用文献学研究方法,对唐氏治疗“血下泄证”的学术观点、治疗理念、方药特色进行了全面而细致的阐发。唐容川在“血下泄证”的论治中强调,(1)下部出血,治金为先,活用宣、润、清三法,多用风药、喜遣荆防;颇爱花粉、多配柴胡;恒赖“泻白”、常伍人参。(2)遵古不泥,每有灼见,多有豁然开朗之论。发挥赤豆当归散与槐角丸,强调升降同调;拓展黄土汤与石莲汤,凸显清补并行。(3)偏爱种仁之属,力遣一药多能之品,水、火、气、血同治,协调配合,环环相扣,别具匠心。     

从《金匮要略》探讨冠心病的证治

冠状动脉粥样硬化性心脏病，其病因是以正气亏虚为主，尤以心、肾、脾三脏的阳气不足为发病的内在因素；在本虚的基础上，实邪干犯，尤其是脏腑功能失调所产生的寒饮、痰浊、血瘀等病理产物痹阻胸阳、影响心脉运行是发病的重要条件。故其病证以本虚标实为特点。在治疗方面，重在辨清标本缓急：标实证要宣通祛邪，除参考运用胸痹心痛篇的治法方药外，特提出肝着、痰饮、瘀血等病证的方药亦可选用；对本虚证的治疗，认为可从《金匮要略》虚劳病篇及其有关内容进行辨证论治，要以补虚为主，或兼以祛邪；对虚实错杂症，应扶正祛邪并施，标本兼顾。     

Phacomatosis Pigmentokeratotica without Extracutaneous Abnormalities: A Case Study Involving a Preterm Baby

Phacomatosis pigmentokeratotica (PPK) is a rare syndrome defined by the association of an organoid nevus occasionally with sebaceous differentiation, a speckled lentiginous nevus, and other extracutaneous anomalies. A preterm male infant of only 830 g at 27 week gestational age had an organoid nevus showing sebaceous differentiation. Also, he had multiple speckled-lentiginous nevus. Correlating the observed clinical presentation with the histopathological findings, the diagnosis of PPK was established. There have been less than 10 cases of PPK without extracutaneous manifestation. We present an uncommon case of a preterm patient with PPK who had no extracutaneous abnormalities.     

Summary on clinical experience of acupuncture treating dry eye syndromes

Dry eye syndromes （DES） refer to discomfort in the eye region, visual disturbance, poor stability of lacrimal film, inflammation of eye surface and its potential injury due to many factors of abnormal lacrimation. Patients with this condition can experience a dry sensation in the eyes, foreign body sensation,