血液系统疾病所致门脉高压症20例临床分析

目的 总结血液系统疾病所致门脉高压的临床特点。方法 回顾性分析我院10年来的血液系统疾病675例（不包括再生障碍性贫血和急性白血病）。结果 有20例诊为门脉高压症，导致门脉高压症的血液病主要是淋巴瘤和骨髓纤维化。结论 与肝硬化导致的门脉高压症相比，血液系统疾病所致门脉高压症的临床特点是：肝脏损害相对轻，血小板降低轻微，脾脏明显增大，肝脏无明显缩小。

Analysis of 20 cases of portal hypertension induced by hematological diseases

Objective To summarize the clinical characteristics of portal hypertension induced by hematological diseases.Methods To review 675 cases with hematological diseases of our hospital in the past ten years (excluding aplastic anemia and acute leukemia) .Results Twenty patients were diagnosed as portal hypertension.Most of these patients suffered from lymphoma or myelofibrosis.Conclusions Compared with the portal hypertension induced by liver cirrhosis,the clinic characteristics of that resulting from hematological disease are as follows:the damage of liver function and the decrease of platelet count is slight;marked splenomegaly is common,while the liver size does not reduce obviously.