| 肺淋巴管平滑肌瘤病 |
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| 引用本文： | 郎建敏,石彦明. 肺淋巴管平滑肌瘤病[J]. 国际呼吸杂志, 2007, 27(10): 740-742 |
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| 作者姓名： | 郎建敏 石彦明 |
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| 作者单位： | 250012,济南,山东大学医学院;250014,济南,千佛山医院呼吸科 |
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| 摘 要： | 淋巴管平滑肌瘤病是一种较为罕见的疾病,由于平滑肌样细胞异常增生导致肺囊肿的形成,导致肺功能进行性的下降,最终死亡。本病主要累及妇女,病因目前尚不清楚,亦无特异性治疗,本文对近来关于该病的报道作一综述。
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| 关 键 词： | 肺淋巴管平滑肌瘤病 结节性硬化症 雌激素 |
| 修稿时间： | 2006-07-21 |
Review of pulmonary lymphangioleiomyomatosis |
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| LANG Jian-min,SHI Yan-ming. Review of pulmonary lymphangioleiomyomatosis[J]. International Journal of Respiration, 2007, 27(10): 740-742 |
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| Authors: | LANG Jian-min SHI Yan-ming |
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| Affiliation: | Medicol College of Shandong University , Jinan 250012, China |
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| Abstract: | Pulmonary lymphangioleiomyomatosis(LAM) is a rare disease that is characterized by proliferation of abnormal smooth muscle-like cells(LAM cells),which leads to the formation of lung cysts leading to progressive loss of lung function and ultimately death.It primarily affects women.The etiology of the disease and the efficacy of currently utilized treatments are unknown.The goal is to review the current understanding of LAM. |
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| Keywords: | Pulmonary lymphangioleiomyomatosis Tuberous sclerosis complex Estrogen |
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