Ⅰ期矫治主动脉弓中断及合并畸形

目的 总结Ⅰ期矫治小儿主动脉弓中断(IAA)及合并畸形的诊治经验.方法 2005年1月至2007年5月诊治主动脉弓中断畸形10例.患儿术前均有反复呼吸道感染史,合并心脏畸形和重度肺动脉高压.其中A型8例,B型2例.采用正中切口Ⅰ期纠治主动脉弓中断和心脏畸形.结果 术后早期死亡1例,另9例随访4～19个月,恢复良好.结论 IAA一旦诊断明确,应尽早治疗,正中开胸Ⅰ期矫治术疗效满意.降主动脉与主动脉弓直接端侧吻合效果较佳.

One stage repair of interrupted aortic arch in 10 patients with associated cardiac anomalies

Objective The purpose of this study was to review our clinical experience of one stage repair of interrupted aortic arch(IAA)with associated cardiac anomalies.Methotis Ten patients(7 male,3 Female)admitted between 2005 to May,2007 were reviewed.All patients suffered from recurrent respiratory infection and severe pulmonary hypertension.The study identified 8 type A cases and 2 type B cases.Midline sternotomy carried out in all patients.Results Nine operations were successful while one patient died.Conclusions Earlier treatment is required for IAA.Midline sternotomy and one stage repair of IAA with cardiac anomalies produce a satisfactory result. End to side anastomosis between the descending aorta and the aorta arch is considered the optimal approach for this surgery.