Portal hypertension and intrahepatic cholestasis in hepatic amyloidosis |
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Authors: | R N Zeijen J P Sels J A Flendrig J W Arends |
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Affiliation: | Department of Internal Medicine, University Hospital Maastricht, The Netherlands. |
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Abstract: | Despite the fact that hepatic involvement is frequently seen in systemic amyloidosis, major clinical symptoms or impaired hepatic functional capacity are rare. We describe a patient with primary hepatic amyloidosis, severe intrahepatic cholestasis and portal hypertension, a combination previously reported only three times in the literature. In case of an unexplained intrahepatic cholestasis or portal hypertension the possibility of amyloidosis should be considered and a Congo red staining should be performed. |
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