听神经病的临床表现和听力学检查结果分析

目的 探讨听神经病的临床表现和听力学特征。方法 分析23例听神经 临床表现、纯音听阈、声导抗、言语听力、听性脑干反应（ABR）和畸变产物耳声发射（DPOAE）检查。结果 听神经病多发于青少年，妇性多于男性。纯音听阈呈轻、中度升高，以双耳对称的上升型听阈图为主。言语识别率显著下降，且与纯音听阈不成比例。同侧、对侧镫骨肌反射引不出，ABR明显异常，DPOAE正常或基本正常。结论 听神经病的临床表现和系统的听力学检查有其显著特征，不仅对认识该病，而且对明确诊断有重要意义。

Analysis of Clinical Findings and Audioloical Result of Auditory Neuropathy

Objective To study the clinical findings and audiological characteristics of auditory neuropathy. Methods Clinical findings, pure tone threshold, acoustic impedance audiometry, speech audiometry, auditory brainstem response (ABR) and distortion product otoacoustic emission( DPOAE) were analyzed in 23 cases of auditory neuropathy. Results The patients were predominantly youngster, female more than male. Pure tone audiometry revealed mainly binaural symmetric upward - sloping audiogram with mild and moderate hearing loss at low frequencies. Speech discrimination score was obviously reduced, which was disproportionately to the pure tone threshold. Ipsilateral and contralateral stapedial reflex were absent. ABR was severely abnor- mal. DPOAIE was normal or nearly normal. Conclusion Clinical findings and systemic audiometry revealed the main characteristics of auditory neuropathy, which could be used not only for the understanding, but also for the diagnosis of this disease.