Late presentation of congenital diaphragmatic hernia in patients with cystic fibrosis |
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| Authors: | Danielle M. Goetz MD Cartland Burns MD Bradley J. Segura MD Daniel J. Weiner MD |
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| Affiliation: | 1. Division of Pulmonary Medicine, Department of Pediatrics, The Children's Hospital of Pittsburgh, Pittsburgh, Pennsylvania;2. Department of Pediatric Surgery, The Children's Hospital of Pittsburgh, Pittsburgh, Pennsylvania |
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| Abstract: | Late presentation of congenital diaphragmatic hernia (CDH) is unusual, especially in patients with cystic fibrosis (CF). To our knowledge, cases of CDH in CF patients and the combined effects on lung function have not been previously described. Here we report two cases of late presenting CDH in CF patients and describe effects on lung function. Late presentation of CDH in CF patients can cause gastrointestinal or respiratory symptoms and requires a high index of suspicion as well as proper interpretation of imaging. In patients with CF and CDH, lung function abnormalities could include obstructive, restrictive defects, or combined defects. Pediatr Pulmonol. 2010; 45:403–405. © 2010 Wiley‐Liss, Inc. |
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| Keywords: | cystic fibrosis congenital diaphragmatic hernia late presentation of congenital diaphragmatic hernia lung function pulmonary function |
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