Nonresectable inflammatory pseudotumor of the porta hepatis

Inflammatory pseudotumors are rare mass lesions often mistaken for malignancy. Currently, only 2 cases of pseudotumors originating from the porta hepatis have been reported in the pediatric literature, and both cases were those of patients older than 30 years. When located in the porta hepatis, pseudotumors are difficult to treat via surgical resection, and other therapeutic options must be considered. We report a pediatric case of inflammatory pseudotumor of the porta hepatis and discuss the different surgical and nonsurgical options used in treating pseudotumors.