| Hallervorden—Spatz病的临床和MRI特点（附2例分析） |
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| 引用本文： | 严新翔,胡鸣一,张玉虎,唐北沙,郭纪锋,汤建光.Hallervorden—Spatz病的临床和MRI特点（附2例分析）[J].中国医学影像学杂志,2005,13(3):167-169. |
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| 作者姓名： | 严新翔 胡鸣一 张玉虎 唐北沙 郭纪锋 汤建光 |
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| 作者单位： | 410008,长沙,中南大学湘雅医院神经内科 |
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| 基金项目： | 国家高技术研究发展计划(863计划),国家自然科学基金,高等学校博士学科点专项科研项目 |
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| 摘 要： | 目的: 探讨苍白球、黑质、红核色素变性的临床和MRI特点.材料和方法: 回顾性分析2例苍白球、黑质、红核色素变性的临床和MRI表现.结果: 主要临床特点: 少年期起病,病情缓慢进展,主要表现为锥体外系症状,均有言语障碍,其中1例有精神障碍、视神经萎缩、步态姿势异常和双侧巴宾斯基征( ); T2 WI均表现为苍白球、黑质等部位对称性低信号,其中1例为"虎眼征".结论: 根据临床和MRI特点可以准确诊断HSD.
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| 关 键 词： | Hallervorden-Spatz病 临床 |
| 修稿时间： | 2004年12月17 |
Characteristics of Hallervorden-Spatz Disease on Clinical and MRI (A Report of 2 Cases) |
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| Yan Xinxiang,Hu Mingyi,ZHANG Yuhu,Tang Beisha,Guo Jifeng,Tang Jianguang.Characteristics of Hallervorden-Spatz Disease on Clinical and MRI (A Report of 2 Cases)[J].Chinese Journal of Medical Imaging,2005,13(3):167-169. |
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| Authors: | Yan Xinxiang Hu Mingyi ZHANG Yuhu Tang Beisha Guo Jifeng Tang Jianguang |
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| Abstract: | Purpose: To explore the clinical and MRI characteristics of Hallervorden-Spatz disease (HSD). Materials and Methods: The clinical and MRI features of 2 patients with HSD were analysed retrospectively. Results: The major clinical features including juvenile onset with slow progression, extrapyramidal syndromes and dysarthria. One case had Gait or postural difficulties, pathologic reflex, optic atrophy and psychiatric symptoms. Significant low signal intensity on T2 WI localized in bilateral globus pallidus and pars compacta of the substantia nigra in two patients, and the "eye of the tiger" sign in one patient. Conclusion: HSD can be diagnosed on the basis of clinical and MRI features. |
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| Keywords: | MRI |
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