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Living Donor Kidney Transplantation in a Patient With Epidermolysis Bullosa: A Case Report |
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| Authors: | S.H.E. Ceuppens H.J.A.N. Kimenai J.I. Roodnat I.R.A.M. Mertens zur Borg J.C. Duipmans J.N.M. IJzermans R.C. Minnee |
| Affiliation: | 1. Department of Surgery, Division of HPB & Transplant Surgery, Erasmus MC, Rotterdam, the Netherlands;2. Department of Internal Medicine, Erasmus MC, Rotterdam, the Netherlands;3. Department of Anaesthesiology, Erasmus MC, Rotterdam, the Netherlands;4. Department of Dermatology, University Medical Center Groningen, the Netherlands |
| Abstract: | Severe recessive dystrophic epidermolysis bullosa is a very rare inherited disease with excessive blisters forming starting at birth. Surgical intervention in this population creates a challenge: preventing formation of new lesions while managing previously scarred tissues.We present a case of a 27-year-old patient with end-stage renal disease caused by rapidly progressive IgA nephropathy. Living donor kidney transplantation was performed under local, spinal and epidural anesthesia.Living kidney transplantation in epidermolysis bullosa patients with end-stage renal disease should not be a contraindication for transplantation and should be considered as a viable and feasible option after careful preparation. |
| Keywords: | Address correspondence to R.C. Minnee Doctor Molewaterplein 40 3015 GD Rotterdam the Netherlands. |
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