Perivascular epithelioid cell tumor in the duodenum: challenge in differential diagnosis |
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Authors: | Zehong Chen Huijuan Shi Jianjun Peng Yujie Yuan Jianhui Chen Wu Song |
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Affiliation: | 1.Department of Gastrointestinal Surgery, The First Affiliated Hospital, Sun Yat-Sen University, 58 Zhongshan 2nd Road, Guangzhou 510080, China;2.Department of Pathology, The First Affiliated Hospital, Sun Yat-Sen University, Guangzhou, China |
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Abstract: | Defined as a family of scarce mesenchymal neoplasm which distinctively co-express melanocytic markers and muscle markers, perivascular epithelioid cell tumors (PEComas) have been reported almost everybody site. Perivascular epithelioid cell tumors-not otherwise specified (PEComas-NOS) arising in the gastrointestinal (GI) tract are still restricted into sporadic case reports. Herein we present a case of GI PEComas-NOS which occurs in the duodenum of a 27-year-old male. Our initial diagnosis tended to gastrointestinal stromal tumor or smooth muscle tumor till the correct diagnosis of perivascular epithelioid cell tumor (PEComa) was established by postoperative pathological examination. We also make a literature review of GI PEComas-NOS and highlight the challenge it brings to the differential diagnosis. |
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Keywords: | Perivascular epithelioid cell tumor duodenum differential diagnosis |
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