Renal transport of aromatic acids in patients with phenylketonuria |
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| Authors: | U. Langenbeck A. Behbehani H. Luthe |
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| Affiliation: | (1) Institute of Human Genetics, Nikolausberger Weg 5a, D-3400 Göttingen, FRG;(2) Children's Hospital, D-3400 Göttingen, FRG;(3) Department of Clinical Chemistry, University of Göttingen, D-3400 Göttingen, FRG |
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| Abstract: | Renal clearance of phenylpyruvic acid is maximal at a plasma concentration of 40–60 µmol/l. This concentration is obtained with plasma phenylalanine concentrations of 1.0–1.2mmol/l, the threshold for separating classical phenylketonuria from phenylketonuria variants. |
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