儿童肝外型门脉高压症的诊治

目的 探讨儿童肝外型门脉高压症的临床分型和治疗经验。方法 回顾30例门脉高压症患儿，肝前性门脉高压13例(43．3％)，肝后性即布加综合征17例(56．7％)。手术治疗20例，保守治疗10例。结果 20例手术治疗患儿治愈好转18例(90％)。其中肝前性门脉高压手术治疗10例，治愈好转10例(100％)；布加综合征手术治疗10例，治愈好转8例(80％)，手术后死亡2例(20％)。保守治疗10例：2例布加综合征人院后死亡，自动出院8例。结论 儿童肝外型门脉高压症临床分型为肝前性和肝后性，以手术治疗为主，肝前性门脉高压症治疗效果和预后明显好于肝后性。

Treatment of Extrahepatic Portal Hypertension in Children

Objective To study the clinical types and treatment of extrahepatic portal hypertension in children. Methods 30 patients were analyzed. 13 cases of the prehepatic portal hypertension(43.3%) and 17 cases of Budd-Chiari Syndrome(56.7%) were treated. 20 cases were treated operatively and 10 nonoperatively. Result 10 cases of the prehepatic portal hypertension and 8 cases of Budd-Chiari Syndrome were treated successfully by surgery. 2 cases of Budd-Chiari Syndrome died after operation. Of nonoperative treatment, 8 cases were cured, but 2 of Budd-Chiari Syndrome died. Conclusion Children's portal hypertension was classified as pre and post hepatic types. Surgical treatment is a good choice. Surgery is more effective for prehepatic portal hypertension than for Budd-Chiari Syndrome.