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胃肠道息肉-皮肤色素沉着-指(趾)甲萎缩综合征1例
引用本文:张萍,张东,李贻奎.胃肠道息肉-皮肤色素沉着-指(趾)甲萎缩综合征1例[J].世界华人消化杂志,2011(4).
作者姓名:张萍  张东  李贻奎
作者单位:北京中医药大学;中国中医科学院西苑医院心内科;中国中医科学院西苑医院实验研究中心;
摘    要:Cronkhite-Canada综合征(Cronkhite-Canada syndrome,CCS)是以胃肠道多发息肉和外胚层三联征两大症候群为主,临床表现为慢性腹泻、腹痛、脱发、皮肤色素沉着、指(趾)甲萎缩脱落等.发病罕见,病因不明,预后较差.本文报道CCS1例,通过病史及内镜检查并结合文献进行分析讨论,提高对CCS的认识.

关 键 词:胃肠道息肉-皮肤色素沉着-指(趾)甲萎缩综合征  胃肠道息肉  外胚层改变  色素沉着  

Cronkhite-Canada syndrome:a report of one case
Ping Zhang,Beijing University of Chinese Medicine,Beijing ,China Dong Zhang.Cronkhite-Canada syndrome:a report of one case[J].World Chinese Journal of Digestology,2011(4).
Authors:Ping Zhang  Beijing University of Chinese Medicine  Beijing  China Dong Zhang
Institution:Ping Zhang,Beijing University of Chinese Medicine,Beijing 100029,China Dong Zhang,Department of Cardiology,Xiyuan Hospital,China Academy of Chinese Medical Sciences,Beijing 100091,China Yi-Kui Li,Research Center,China
Abstract:Cronkhite-Canada syndrome(CCS) is a rare clinic entity of unknown etiology and has poor prognosis,characterized by gastrointestinal polyposis with ectodermal changes.Main clinical manifestations include chronic diarrhea,abdominal pain,alopecia,skin pigmentation,and nail changes.Here,we report a case of CCS in a 50-year-old male and review the relevant literature.
Keywords:Cronkhite-Canada syndrome  Gastrointestinal polyposis  Ectodermal changes  Skin pigmentation  
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