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子宫血管平滑肌脂肪瘤1例及文献复习
引用本文:芮佳敏 黄彩虹 姜舟 崔树娜 李士华. 子宫血管平滑肌脂肪瘤1例及文献复习[J]. 国际医药卫生导报, 2022, 28(21): 3029-3031. DOI: 10.3760/cma.j.issn.1007-1245.2022.21.013
作者姓名:芮佳敏 黄彩虹 姜舟 崔树娜 李士华
作者单位:1扬州大学医学院,扬州 225000;2扬州大学附属医院病理科,扬州 225000;3扬州大学附属医院妇产科,扬州 225000
基金项目:江苏省研究生科研与实践创新计划(SJCX21-1648)
摘    要:血管平滑肌脂肪瘤(AML)是血管周上皮样细胞肿瘤(PEComa)中的一种,其特征是良性平滑肌细胞、脂肪细胞和血管呈不同比例存在,发病率较低,尚缺乏统一的指南或共识。本文报道了1例子宫血管平滑肌脂肪瘤的诊疗经过,同时通过文献复习的方式探讨PEComa的临床表现、诊断、分子机制、治疗及预后。

关 键 词:血管平滑肌脂肪瘤  血管周上皮样细胞肿瘤  子宫肿瘤  
收稿时间:2022-06-30

One case of uterine angiomyolipoma and literature review
Rui Jiamin,Huang Caihong,Jiang Zhou,Cui Shuna,Li Shihua. One case of uterine angiomyolipoma and literature review[J]. International Medicine & Health Guidance News, 2022, 28(21): 3029-3031. DOI: 10.3760/cma.j.issn.1007-1245.2022.21.013
Authors:Rui Jiamin  Huang Caihong  Jiang Zhou  Cui Shuna  Li Shihua
Affiliation:1 Medical College, Yangzhou University, Yangzhou225000, China; 2 Department of Pathology, The Affiliated Hospital ofYangzhou University, Yangzhou 225000, China; 3 Department ofGynecology and Obstetrics, The Affiliated Hospital of Yangzhou University,Yangzhou 225000, China
Abstract:Angiomyolipoma (AML) is a kind of perivascularepithelioid cell tumor (PEComa). It is a benign tumor composed of variedproportions of blood vessels, adipocytes, and epithelioid or spindled smoothmuscle cells. The incidence of AML is low, and there is no guideline orconsensus. In this study, we report the diagnosis and treatment of a woman withuterine AML. Meanwhile, the clinical manifestations, diagnosis, molecularmechanism, treatment, and prognosis of PEComa are discussed through literaturereview.
Keywords:Angiomyolipoma  Perivascular epithelioid cell tumor  Uterine neoplasms  
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