人工耳蜗植入在大前庭水管综合征患者中的应用

目的 探讨大前庭水管综合征患者人工耳蜗植入方法及手术前后听力评估和术后言语康复效果.方法 回顾性分析2005～2008年于我科确诊的大前庭水管综合征22例行人工耳蜗植入患者的临床资料,所有患者均经乳突面隐窝进路行人工耳蜗植入,并将其中22例患者植入后听力情况与22例耳蜗发育正常的人工耳蜗植入者(对照组)进行比较.结果 22例大前庭水管综合征患者有3例术中出现严重井喷,15例术中耳蜗钻孑L后见外淋巴液出现不同程度的波动,异常情况共占81.8%,但术中电极完全插入耳蜗,术后无面瘫及脑脊液漏现象发生,术后听阈与耳蜗结构正常植入患者无明显区别.经过超过半年的言语康复训练,所有患者的听力及言语能力均有不同程度提高.结论 人工耳蜗适用于大前庭水管综合征患者,术前应进行全面的听力学及影像学评估.

Abstract：

Objective To evaluate the hearing and speech recognition in patients with large vestibular aqueduct syndrome undergoing multi-channel cochlear implantation. Methods From 2005 to 2008, multi-channel cochlear implantation surgeries were performed in 22 patients with large vestibular aqueduct syndrome. All the patients received multi-channel cochlear implantation through transmastoid facial recess approach. The postoperative outcomes of the patients were compared with those of 22 patients with non-malformed cochlear. Result Severe gusher occurred in 3 cases during the implantation, and perilymph fluctuation was found in another 15 cases, with a rate of anomalies of 81.8%. All the electrodes were totally inserted into the cochlear, and no facial paralysis or cerebrospinal fluid leakage occurred after the operation. The hearing threshold in these patients was similar to that in patients with normal cochlear receiving the implantation. After speech rehabilitation for over 6 months, all the patients showed improved hearing and verbal ability. Conclusion Multi-channel cochlear implantation can be performed in patients with large vestibular aqueduct syndrome, but preoperative hearing assessment and radiographic examinations should be performed.

Cochlear implantation in patients with large vestibular aqueduct syndrome

Objective To evaluate the hearing and speech recognition in patients with large vestibular aqueduct syndrome undergoing multi-channel cochlear implantation. Methods From 2005 to 2008, multi-channel cochlear implantation surgeries were performed in 22 patients with large vestibular aqueduct syndrome. All the patients received multi-channel cochlear implantation through transmastoid facial recess approach. The postoperative outcomes of the patients were compared with those of 22 patients with non-malformed co...