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成人线状IgA大疱性皮病1例
引用本文:郭生红,李薇.成人线状IgA大疱性皮病1例[J].中国皮肤性病学杂志,2011,25(9).
作者姓名:郭生红  李薇
作者单位:四川大学华西医院皮肤性病科,四川成都,610041
摘    要:患者女,43岁。面颈部及躯干反复出现红斑和水疱7月。皮肤科情况:面颈部及躯干泛发水肿性红斑、丘疹和张力性小水疱,呈环状排列。皮损组织病理示:表皮下水疱,疱内及真皮可见大量嗜酸性粒细胞浸润,真皮层有少许中性粒细胞等炎性细胞浸润。直接免疫荧光见基底膜带IgA呈线状沉积。诊断:成人线状IgA大疱性皮病。予氨苯砜治疗2周,起效快,疗效好。

关 键 词:线状IgA大疱性皮病

A Case of Linear lgA Bulous Dermatosis
GUO Sheng-hong,LI Wei.A Case of Linear lgA Bulous Dermatosis[J].The Chinese Journal of Dermatovenereology,2011,25(9).
Authors:GUO Sheng-hong  LI Wei
Institution:GUO Sheng-hong,LI Wei(Department of Dermatovenereology,West China Hospital of Sichuan University,Chengdu 610041,China)
Abstract:A 43-year-old woman presented with a 7-month-history erythema and blisters involved face,neck and trunk.The lesions were erythema,papules and circular tense blisters.Histopathologic examination showed a subepidermal blister with prominent neutrophils infiltrate and eosinophilic granulocytes in the papillary dermis.Direct immunofluorescence showed continuous linear deposits of IgA in the basement membrane zone.A diagnosis of LABD was made.After two-week treatment with dapsone,marked improvement was observed.
Keywords:Linear IgA bullous dermatosis  
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