A case of Marfan syndrome with recurrent bilateral pneumothorax and anuloaortic ectasia |
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| Authors: | N Yoshimura T Asada H Matsuda H Nohara T Higami M Nishiwaki N Mukohara M Chibana K Ogawa |
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| Affiliation: | Division of Cardiovascular Surgery, Hyogo Brain and Heart Center at Himeji. |
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| Abstract: | A 17-year-old male patient with Marfan syndrome was admitted due to recurrent bilateral pneumothorax which had recurred totally 11 times during the past 3 years. For the treatment of obstinately continuing right pneumothorax resection of bullae in combination with pleuropexy using OK 432 was effective. Two months thereafter Bentall operation with a composite graft consisting of a woven Dacron tube and a Bj?rk-Shiley 27 mm aortic valve prosthesis was performed for his anuloartic ectasia. Left pneumothorax recurred 2 weeks after Bentall operation. But it was treated successfully with OK 432 injection into the left pleural cavity. Now, he is doing well as a student. |
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