CT features of extra-abdominal aggressive fibromatosis

Objective: To analyze the CT characters of extra-abdominal aggressive fibromatosis,in order to achieve more information about the disease and to improve the diagnostic accuracy.Methods: The CT appearances of extra-abdominal aggressive fibromatosis in nine cases were reviewed.All the cases were confirmed by operation and pathology.Results: In the nine cases of extra-abdominal aggressive fibromatosis,seven tumors were located in soft tissue(including five in chest wall,two in neck and one in thigh) and two in bone(sacrum and maxillary respectively).On pre-contrast CT images,seven tumors in soft tissue showed equal or mild lower density than muscle,with bone destruction in three cases.On enhanced CT images,three cases showed mild to moderate enhancement,and four showed significantly enhancement.Aggressive fibromatosis of bone were expansive lytic with bony rim in one case and trabecular bone in the other case.Conclusion: Aggressive fibromatosis is a rare soft tissue tumor.It has certain characteristic performance of CT,yet final diagnosis should be based on histopathology.