肺泡蛋白沉积症影像学诊断

目的：探讨肺泡蛋白沉积症的影像学诊断。材料与方法：搜集肺泡蛋白沉积症４例,其中３例由支纤镜检及肺泡灌洗术正实,１例尸检证实。均摄有胸部正侧位片,其中１例进行了Ｃ画内外相关骸尸检病理所见,对其影像学表现进行回顾性分析并探讨其病理基础。结果：该病依病程长短可分别具有下列不同的影像学表现：（１）弥散分布的非肿瘤性腺泡结节,为较早期表现;（２）弥温性斑片状阴影与磨玻璃影与磨玻璃影,ＣＴ扫描病灶常呈地图样分

Imaging Diagnosis of Pulmonary Alveolar Proteinosis

Objective: To Study the imaging diagnosis of pulmonary alveolar proteinosis (PAP). Materials and Methods: Imaging features of 4cases with PAP were analyzed retrospectively, of which 3 cases were histologically proved by fiberoptic bronchoscopy and bronchoalveolar lavage and1 case by autopsy. Chest X-ray film was performed in all cases and CT scan in one. Results:With the developing of the disease, the following ima-ging features were seen. (1) Diffuse, ill-defined acinus nodule, an early sign. (2) Diffuse patchy shadows and ground glass appearance, distibutedgeographically on CT. (3) Butterfly sign, usually seen in prolonged cases. (4) Air-brochogram sing. (5) Consolidation or groud glass shadow withreticular background, creating the typical "crazy-paving" appearances. Conclusion: Carefully distinguishing the X-ray and CT appearances, confirm-ing of air-space lesion, observing the shape and distribution of the lesion, and taking the clinical history into consderation together, a reliable diag-nosis can be made, needn' t doing bronchoscopy or TNB.