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MRI对脂质沉积性肌病的评估价值
引用本文:郑贤应,慕容慎行,李银光,倪希和,蔡江萍. MRI对脂质沉积性肌病的评估价值[J]. 中国组织工程研究与临床康复, 2003, 7(5): 854
作者姓名:郑贤应  慕容慎行  李银光  倪希和  蔡江萍
作者单位:IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China
摘    要:INTRODUCTIONLipidstoragemyopathybelongstoinflammationofmusclecellscausedbyselfimmunity.(lipidstoragemyopathy,LSM).DomesticresearchesaboutitsevaluationwithMRIwereunavailable.Ourob-jectivewastoinvestigateMRIfindingsofLMIanditsvalueintheevaluationofLSM.MATERIALSANDMETHODSMaterials9LSMpatientsadmittedfromApril1998toApril2002werein-cludedinourstudy.Thesepatientsinclude5menand5womenaging4-36years(meanage:24.9years).Courseofdiseasevariedfrom9mont…


Value of MRI in the evaluation of lipid storage myopathy
Zheng Xianying,Murong Shenxing,Li Yinguang,Ni Xihe,Cai JiangpingZheng Xianying,Murong Shenxing,Li Yinguang,Ni Xihe,Cai Jiangping,Intraneural Department,First Affiliated Hospital,Fujian Medical University,Fuzhou ,Fujian Province,China. Value of MRI in the evaluation of lipid storage myopathy[J]. Journal of Clinical Rehabilitative Tissue Engineering Research, 2003, 7(5): 854
Authors:Zheng Xianying  Murong Shenxing  Li Yinguang  Ni Xihe  Cai JiangpingZheng Xianying  Murong Shenxing  Li Yinguang  Ni Xihe  Cai Jiangping  Intraneural Department  First Affiliated Hospital  Fujian Medical University  Fuzhou   Fujian Province  China
Affiliation:Intraneural Department, First Affiliated Hospital, Fujian Medical University, Fuzhou 350001, Fujian Province, China
Abstract:AIM: To investigate the magnetic resonance imaging (MRI) findings of lipid storage myopathy(LSM),evaluate the clinical value of MRI for LSM. METHODS:Eight cases with LSM biopsy proved underwent MRI of pelvis and thigh, spin echo sequence,fast spin echo sequence and short tau inversion recovery(STIR) were utilized.RESULTS:The signal intensity of diseased muscle of 8 cases with LSM was hyperintense on T2 weighted images (T2WI) and T1 weighted images (T1WI),and hyperintense signal intensity on T2WI and iso intense on T1WI was seen on 2 patients as well . CONCLUSION:MRI can provide objective data for clinical diagnosis,therapeutic evaluation and follow up.It can also help to decide the accurate localizations for biopsies.
Keywords:lipidoses  muscular disease  magnetic resonance imaging
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