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MRI对脂质沉积性肌病的评估价值
引用本文:郑贤应,慕容慎行,李银光,倪希和,蔡江萍.MRI对脂质沉积性肌病的评估价值[J].中国组织工程研究与临床康复,2003,7(5):854.
作者姓名:郑贤应  慕容慎行  李银光  倪希和  蔡江萍
作者单位:IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital,IntraneuralDepartmentFirstAffiliatedHospital FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China,FujianMedicalUniversity,Fuzhou350001,FujianProvince,China
摘    要:INTRODUCTIONLipidstoragemyopathybelongstoinflammationofmusclecellscausedbyselfimmunity.(lipidstoragemyopathy,LSM).DomesticresearchesaboutitsevaluationwithMRIwereunavailable.Ourob-jectivewastoinvestigateMRIfindingsofLMIanditsvalueintheevaluationofLSM.MATERIALSANDMETHODSMaterials9LSMpatientsadmittedfromApril1998toApril2002werein-cludedinourstudy.Thesepatientsinclude5menand5womenaging4-36years(meanage:24.9years).Courseofdiseasevariedfrom9mont…


Value of MRI in the evaluation of lipid storage myopathy
Zheng Xianying,Murong Shenxing,Li Yinguang,Ni Xihe,Cai JiangpingZheng Xianying,Murong Shenxing,Li Yinguang,Ni Xihe,Cai Jiangping,Intraneural.Value of MRI in the evaluation of lipid storage myopathy[J].Journal of Clinical Rehabilitative Tissue Engineering Research,2003,7(5):854.
Authors:Zheng Xianying  Murong Shenxing  Li Yinguang  Ni Xihe  Cai JiangpingZheng Xianying  Murong Shenxing  Li Yinguang  Ni Xihe  Cai Jiangping  Intraneural
Institution:Intraneural Department, First Affiliated Hospital, Fujian Medical University, Fuzhou 350001, Fujian Province, China
Abstract:AIM: To investigate the magnetic resonance imaging (MRI) findings of lipid storage myopathy(LSM),evaluate the clinical value of MRI for LSM. METHODS:Eight cases with LSM biopsy proved underwent MRI of pelvis and thigh, spin echo sequence,fast spin echo sequence and short tau inversion recovery(STIR) were utilized.RESULTS:The signal intensity of diseased muscle of 8 cases with LSM was hyperintense on T2 weighted images (T2WI) and T1 weighted images (T1WI),and hyperintense signal intensity on T2WI and iso intense on T1WI was seen on 2 patients as well . CONCLUSION:MRI can provide objective data for clinical diagnosis,therapeutic evaluation and follow up.It can also help to decide the accurate localizations for biopsies.
Keywords:lipidoses  muscular disease  magnetic resonance imaging
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