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产前超声心动图诊断胎儿左心室发育不良综合征
引用本文:姜立新,沈国芳,应涛,胡兵.产前超声心动图诊断胎儿左心室发育不良综合征[J].中国医学影像技术,2010,26(12):2346-2349.
作者姓名:姜立新  沈国芳  应涛  胡兵
作者单位:上海交通大学附属第六人民医院超声医学科,上海,200233
摘    要:目的 探讨胎儿超声心动图诊断左心室发育不良综合征(HLHS)的临床价值。方法 对18胎HLHS胎儿的临床资料进行回顾性研究,分析其超声心动图特征。结果 18胎HLHS胎儿的超声心动图结果:①心尖四腔心切面:左心室小、心室发育不良。8胎二尖瓣及主动脉瓣闭锁,且左心室重度发育不良;5胎二尖瓣闭锁合并主动脉瓣狭窄及主动脉缩窄;3胎二尖瓣狭窄伴主动脉瓣狭窄及主动脉弓缩窄;2胎二尖瓣狭窄伴主动脉瓣闭锁及主动脉弓缩窄。②三血管切面:主动脉内径明显小于肺动脉,主动脉与肺动脉内径比值为0.25~0.40,平均0.38±0.18,主动脉横弓与动脉导管、肺动脉血流方向相反。③胸骨旁四腔心切面:6胎房间隔增厚,未显示房间隔穿隔血流。12胎胎儿卵圆孔径偏小、显示房间隔左向右分流。结论 胎儿超声心动图可早期诊断胎儿HLHS,结合染色体检查对围生期的监测和临床处理有重要意义。

关 键 词:左心室发育不良综合征  胎儿  超声心动描记术
收稿时间:2010/8/16 0:00:00
修稿时间:9/4/2010 12:00:00 AM

Prenatal echocardiography in diagnosis of fetal hypoplastic left heart syndrome
JIANG Li-xin,SHEN Guo-fang,YING Tao and HU Bing.Prenatal echocardiography in diagnosis of fetal hypoplastic left heart syndrome[J].Chinese Journal of Medical Imaging Technology,2010,26(12):2346-2349.
Authors:JIANG Li-xin  SHEN Guo-fang  YING Tao and HU Bing
Institution:Department of Ultrasound in Medicine, the Sixth People's Hospital Affiliated to Shanghai Jiao Tong University, Shanghai 200233, China;Department of Ultrasound in Medicine, the Sixth People's Hospital Affiliated to Shanghai Jiao Tong University, Shanghai 200233, China;Department of Ultrasound in Medicine, the Sixth People's Hospital Affiliated to Shanghai Jiao Tong University, Shanghai 200233, China;Department of Ultrasound in Medicine, the Sixth People's Hospital Affiliated to Shanghai Jiao Tong University, Shanghai 200233, China
Abstract:
Keywords:Hypoplastic left heart syndrome  Fetus  Echocardiography
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