T-cell lymphoma with von Hippel-Lindau disease: a rare case report and review of literature |
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| Authors: | Li-Hong Lou Hua Shen Jun Lin Yi-Wen Yan Yan Peng Jian-Hong Lu Qu Xu Hai-Qiong Jiang |
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| Affiliation: | 1International Medical Care Center, Shanghai General Hospital, Shanghai Jiao Tong University, Shanghai 200080, China;2Department of Pathology, Shanghai General Hospital, Shanghai Jiao Tong University, Shanghai 200080, China |
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| Abstract: | von Hippel-Lindau disease (VHLD) comprises a series of complicated clinical manifestations. We hereby described a unique case of co-existing T-cell lymphoma (TCL) and confirmed VHLD. The symptoms in this 42-year-old male included fever and pancytopenia. Overall tests and examination made an infectious process unlikely. The results of bone marrow biopsy confirmed the diagnosis. The purposes we described this case were to probe into the relationship between TCL and VHLD, which was not mentioned in previously literature. Combination of clinical, radiological, immunophenotypic, pathological, and genetic data plays an important role in improving the rate of diagnosis, particularly in the challenge for diagnosis of T cell non-Hodgkin lymphoma. |
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| Keywords: | von Hippel-Lindau disease T-cell lymphoma hematological neoplasm |
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