烟雾病18例的临床表现及影像学分析探讨

目的 分析烟雾病的临床特征及影像学表现.方法 回顾性总结分析南京军区南京总医院2007年4月～2009年12月内所收治的18例MMD患者的临床症状、影像学检查结果及诊断价值.结果 8例患者影像学检查有不同部位颅内出血,以脑实质和脑室出血为主.CTA、MRA及DSA检查示16例颅内异常血管网形成,累及血管为颈内动脉系统伴颈外系统病变、基底动脉、大脑后动脉、椎动脉.结论 在排除其他原因所致脑出血后,CT可做初步诊断,CTA、MRA可做为本病进一步检查的首选,但确诊仍需行DSA.

The clinical features and imagery analyzation of MMD on 18 cases

Objective To analyze the clinical features and imagery display of moyamoya disease （ MMD ） o Methods Retrospective analysis the imageologic results,diagnostic values of MMD on 18 cases which were treated in Nanjing General Hospital of Nanjing Military Command during April 2007 - December 2009. Results Imaging studies of 18 cases showed that hemorrhage in different sites ventricular hemorrhage was more common, on CTA, MAR and DSA, the stenosis of internal carotid arteries and the middle cerebral arteries were observed, and collateral vessels were revealed in cerebral hemispheres. Conclusion After the exclusion of other causes induced brain hemorrhage, CT can suggeset the initial diagnosis of the disease. CTA,MRA can be first to next check of MMD, but find a diagnosis should depend on DSA.