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先天性心脏病合并永存左上腔静脉及右上腔静脉缺如畸形的九例报告
引用本文:潘世伟,萧明第,刘迎龙,朱晓东,吴清玉. 先天性心脏病合并永存左上腔静脉及右上腔静脉缺如畸形的九例报告[J]. 中国循环杂志, 1995, 0(12)
作者姓名:潘世伟  萧明第  刘迎龙  朱晓东  吴清玉
作者单位:中国医学科学院,中国协和医科大学心血管病研究所,中国协和医科大学阜外心血管病医院
摘    要:本文报道了在施行先天性心脏病心内直视手术中,发现永存左上腔静脉合并右上腔静脉缺如9例。其中法乐四联症、室间隔缺损各3例;房间隔缺损、右室双出口、单心室一单心房各1例。手术死亡2例。本文对永存左上腔静脉合并右上腔静脉缺如的诊断、术中左上腔静脉的处理、心律的变化特点及其预防与诊治,进行了讨论。

关 键 词:先天性心脏病,永存左上腔静脉,右上腔静脉缺如

ABSENT RIGHT SUPERIOR VENA CAVA WITH PERSISTENT LEFT SUPERIOR VENA CAVA
Pan Shi-Wei , Xiao Ming-Di, Liu Ying-Long,et al.. ABSENT RIGHT SUPERIOR VENA CAVA WITH PERSISTENT LEFT SUPERIOR VENA CAVA[J]. Chinese Circulation Journal, 1995, 0(12)
Authors:Pan Shi-Wei    Xiao Ming-Di   Liu Ying-Long  et al.
Affiliation:Pan Shi-Wei , Xiao Ming-Di, Liu Ying-Long, et al.
Abstract:Among 326 patients of persistent left superior vena cava (PLSVC) , 9 were found to have associated with absence of right superior vena cava(RSVC) during intracardiac operation. 2 of them died after operation. Because of the rarity of this congenital anomaly (0. 47/000)the clinical and surgical implications were discussed.
Keywords:Congenital heart disease  Persistent left superior vena cava  Absent right superior vena cava  
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