Abstract: | Hearing measurements were made on both hospital samples and samples drawn from the general population in Nigeria. Poorer hearing levels were associated with Nigerian ataxic neuropathy, and a significant correlation was demonstrated between a score of overall clinical neurological deficit and the hearing levels for 250, 500 and 1 000 Hz. A variety of audiometric patterns was observed and the topodiagnostic tests indicated the occurrence of both receptor organ and neuronal lesions. Temporary threshold drift appeared to be associated with untreated cases of the condition. The study indicated that the prevalence of Nigerian Ataxic Neuropathy is probably much higher than hitherto assumed. |