肺淋巴管平滑肌增生症的腹部CT表现

目的探讨肺淋巴管平滑肌增生症腹部病变的CT表现。方法回顾性分析7例经病理证实的肺淋巴管平滑肌增生症，7例均作腹部CT扫描，对其腹部CT表现进行研究分析。结果7例患者中6例有腹部阳性表现：肾血管平滑肌脂肪瘤2例，其中1例合并胸导管增大、胸腔积液；腹膜后淋巴结肿大2例，合并腹水、胸腔积液1例；肝脏血管平滑肌脂肪瘤1例；腹膜后淋巴管肌瘤合并子宫肌瘤1例。结论肺淋巴管平滑肌增生症可并发腹部多脏器病变，CT扫描对发现和诊断其腹部病变具有重要意义。

Abdominal CT findings of 7 patients with pulmonary lymphgiomyomatosis

Objective To describe and study the abdominal computed tomographic(CT)findings in patients with pulmonary lymphangiomyomatosis(PLAM). Methods Abdominal CT was performed in all the seven cases with histopathologically proved pulmonary lymphangiomyomatosis, then the abdominal CT findings were described. Results Six of these 7 cases had positive abdominal CT findings:renal angiomyolipoma in 2 cases,one of these patients also had dilatation of the thoracic duct and pleural effusion;enlarged abdominal lymph nodes in 2 cases, one patient also had ascites and pleural effusion.Others findings included lymphangiomyoma and uterine tumor in one, hepatic angiomyolipoma in one. Conclusion PLAM can be complicated by abdominal multiorganic pathology frequently,abdominal examination in patients with PLAM must be valued greatly,CT examination is of important significance to discover and diagnosis abdominal pathology.