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Severe pulmonary arterial stenoses in Conradi-Hünermann disease |
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| Authors: | E. Trowitzsch R. Richter W. Eisenberg H. C. Kallfelz |
| Affiliation: | (1) The Children's Hospital, Department of Pediatric Cardiology, Medical School of Hannover, Konstanty-Gutschow-Str., D-3000 Hannover 61, Federal Republic of Germany;(2) Department of Pediatric Oncology, The Children's Hospital, Medical School of Hannover, D-3000 Hannover, Federal Republic of Germany;(3) Children's Hospital of Herford, D-4900 Herford, Federal Republic of Germany |
| Abstract: | A 5-month-old male infant with chondrodystrophia punctata type Conradi-Hünermann showed electrocardiographically an enormous enlarged right ventricle with signs of supra-systemic pressure was found. No other intracardiac defects could be seen. Angiography showed severe peripheral pulmonary arterial stenoses of both main arteries. Balloon-dilatation or surgical intervention was supposed to have no beneficial effect. At the age of 6 months the patient died. |
| Keywords: | Chondrodysplasia punctata Conradi-Hü nermann Pulmonary arterial stenosis |
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