进行性半面萎缩症的综合外科矫治术

目的 评价综合应用正颌外科、颌骨牵引成骨技术和去表皮肩胛游离皮瓣移植术矫治进行性半面萎缩畸形的疗效与可行性.方法 5例进行性半面萎缩畸形,轻度畸形的1例行去表皮肩胛游离皮瓣移植充填术及同期行颏成形术;中度畸形的2例,一期行上颌Le Fort I型截骨术,双侧下颌升支矢状劈开截骨术和颏成形术,3～6个月后行去表皮肩胛游离皮瓣移植充填术;重度畸形的2例,一期行患侧下颌升支和上颌牙骨段的同期牵引成骨术,3～4个月后取出牵引器的同时行去表皮肩胛游离皮瓣移植充填术.结果 5例患者正颌外科及牵引成骨均效果良好,去表皮肩胛游离皮瓣均成活,患者面部对称性得到明显改善.结论 ①进行性半面萎缩症的程度与发病年龄密切相关,发病年龄越小,畸形越严重.②综合应用正颌外科、颌骨牵引成骨技术和去表皮肩胛游离皮瓣移植充填术,可有效矫治进行性半面萎缩畸形的软、硬组织复合畸形.

Correction of progressive hemifacial atrophy by orthognathic surgical procedures combined distraction osteogenesis and scapular flap transplantation:5 cases report

OBJECTIVE: To evaluate the feasibility and the therapeutic effect of orthognathic surgical procedures combined distraction osteogenesis and scapular flap for correction of progressive hemifacial atrophy. METHODS: 5 cases with progressive hemifacial atrophy were treated. 1 mild case was treated with microsurgical de-epithelia scapular flap (MDSF) and genioplasty in one stage. The 2 moderate cases were treated with Le Fort 1 osteotomy following by sagittal split ramus osteotomy and genioplasty at the first stage. 3 - 6 months later, the MDSFs were used for augmentation. 2 sever cases were treated with bimaxillary distraction osteogenesis on the affected side. 3 - 4 months later, the distraction devices were removed and MDSFs were transplanted. RESULTS: The facial asymmetry was obviously improved. The orthognathic procedures and distraction osteogenesis achieved good therapeutic effect. All the MDSFs were survived. CONCLUSIONS: The progressive hemifacial atrophy can result in very severe deformity when it occurs in very young age. The combined deformity of bone and soft tissue can be effectively corrected by orthognathic procedures combined with distraction osteogenesis and scapular flap transplantation.