Congenital Rosai–Dorfman disease presenting with anemia,thrombocytopenia, and hepatomegaly |
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Authors: | CP Chow MBBS MRCPCH HK Ho MBBS MRCP GCF Chan MD FRCPCH SY Ha MBBS FRCPCH |
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Institution: | Department of Paediatrics and Adolescent Medicine, Queen Mary Hospital, Hong Kong, China |
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Abstract: | Rosai–Dorfman disease (RDD) is a rare entity of non‐Langerhans cell histiocytoses (non‐LCH) which usually presents with bilateral painless cervical lymphadenopathy. We describe a neonate with RDD who presented with anemia, thrombocytopenia and hepatomegaly. He recovered spontaneously with conservative management. This represents an atypical presentation of RDD. Conservative management with close monitoring can be adopted for some with systemic involvement. Pediatr Blood Cancer 2009;52:415–417. © 2008 Wiley‐Liss, Inc. |
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Keywords: | anemias hepatomegaly Rosai– Dorfman disease sinus histiocytosis with massive lymphadenopathy thrombocytopenia |
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