Unilateral congenital corneal staphyloma with retinal neovascularization

I present the light microscopic and ultrastructural findings in an unusual case of unilateral congenital corneal staphyloma. The anterior segment exhibited features of extensive Peters' anomaly whereas the posterior segment showed marked preretinal neovascularization and lack of axons as well as outer segments. These retinal changes might be secondary due to raised intraocular pressure and traction phenomena, but the complexity and extent of the described malformation argue against this.Presented at the 29th Annual Meeting of the European Ophthalmic Pathology Society, Coimbra, Portugal, June 1990