Gorham—Stout综合征的X线诊断

目的：探讨Gorham-Stout综合征的X线表现特点，以期提高对本病X线诊断的认识水平，有助于与其他溶骨性改变的疾患鉴别。材料与方法：3例经病理证实的Gorham-Stout综合征，其中单发于肋骨2例，肋骨、肱骨、肩胛骨多发1例。回顾性研究其X线表现，结合国内外文献资料，分析其X线诊断及鉴别诊断要点。结果：3例均呈进行性大片骨质溶解破坏；长骨破坏区残端消尖变细，无骨膜反应及新骨形成，无软组织肿块，病理性骨折不愈合等X线征象，具有一定病变特征。结论：Gorham-Stout综合征的X线表现具有特征性。结合病史特点，X线可提示本病的诊断，但须排除其他可引起溶骨性改变的疾病。

X-ray Diagnosis of Gorham-Stout Syndrome (An Analysis of Three Cases with Literature Review)

Objective To make a further understanding of the radiologic characteristics of Gorhan-Stout syndrome.Materials and Methods The radiographic findings in 3 cases with pathologically-proved Gorhan-Stout syndrome were retrospectively reviewed. The disease only affected the ribs in 2 cases, while multiple regions were involved in one case.Results The characteristic X-ray features of Gorhan-Stout syndrome were as follows: spontaneous, progressive and osteolytic destruction, disappearing of bone in great quantity, taping of the bone remnants, absence of new bone formation or soft tissue mass, pathological fractures hardly to fuse.Conclusion Gorhan-Stout syndrome has some certain X-ray characteristics which are very helpful in differentiation with other osteolytic diseases.