Extranodal Rosai-Dorfman disease presenting as an isolated epibulbar mass |
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Authors: | Maheshwari Rajat Shekde Satish |
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Affiliation: | Shri Ganapati Netralaya, Orbit, Lacrimal and Ophthalmic Plastic Service, Jalna-431 203, Maharashtra, India |
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Abstract: | Rosai-Dorfman disease is a rare idiopathic disorder characterized by painless lymphadenopathy with cervical involvement in more than 80% cases. We report a case of Rosai-Dorfman disease presenting as an isolated epibulbar mass in a healthy young adult male. Epibulbar involvement in Rosai-Dorfman disease is a rare presentation as can be seen from a review of all literature. The presentation, differential diagnosis and treatment are discussed. |
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Keywords: | Epibulbar mass Rosai-Dorfman disease |
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