Total correction of double-outlet right ventricle, atrial septal defect, pulmonic stenosis with a concordant atrioventricular relationship, dextrocardia and situs inversus

Surgical correction of a rare type of double-outlet right ventricle was successfully carried out in a 20-year-old man. The malformation was associated with atrial septal defect, ventricular septal defect, pulmonic stenosis, a concordant atrioventricular relationship, and dextrocardia with situs inversus. A Teflon patch was sutured as a baffle in the right ventricle to direct blood that had passed from the left ventricle through the ventricular septal defect out through the aorta. The infundibular obstruction was resected, a pulmonic commissurotomy performed and the atrial septal defect closed. The patient made an uneventful recovery and was well at follow-up 1 year later.