外耳道腺样囊性癌6例

目的：探讨外耳道腺样囊性癌的临床及病理特点，以提高诊断和治疗水平。方法：回顾性分析6例外耳道腺样囊性癌患者的临床表现、治疗及随访结果，其中5例行颞骨次全切除术（含外耳道全切除），1例行外耳道后下壁广泛切除及鼓室成形术。结果：全部患者术后随访8～21个月无复发。结论：外耳道腺样囊性癌生长缓慢，可长期带瘤生存，但远期预后不佳，首次治疗应该采用扩大根治性手术以提高治愈率。

Six cases of adenoid cystic carcinoma in external auditory canal

Objective:By investigating the clinical and pathological features of adenoid cystic carcinoma in external auditory canal, we can improve our ability of diagnosis and treatment.Method:A retrospective analysis was performed on 6 patients with adenoid cystic carcinoma in external auditory canal, including clinical manifestations, the therapy as well as the follow-up results.All cases underwent subtotal temporal bone resection or other aggressive surgical encision.Result:All cases were alive for a period from 8 to 21 months after subtotal temporal bone resection or other aggressive surgical excision, without any signs of regional lymph node metastasis and distal metastasis.Conclusion:Adenoid cystic carcinoma in external auditory canal grows slowly, so patients can live with the tumor for a long time. But the long-term prognosis is poor. It is necessary to manipulate aggressive surgical excision at the first time to improve cure rate.