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Evaluation of respiratory complications in patients with X-linked and autosomal recessive agammaglobulinemia
Authors:Saba Fekrvand  Reza Yazdani  Peter Olbrich  Gholamreza Azizi  Rohola Shirzadi  Mohammadreza Modaresi  Mahsa Sohani  Samaneh Delavari  Arash Kalantari  Mansoureh Shariat  Alireza Shafiei  Na Lu  Gholamreza Hassanpour  Maziar Rahimi Hajiabadi  Parisa Ashournia  Anahita Razaghian  Marzieh Asgharyan  Zahra Shahraki-Ghadimi  Roja Rouhani  Fatemeh Hoda Fallah  Nima Rezaei  Hassan Abolhassani  Asghar Aghamohammadi
Affiliation:1. Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran;2. Sección de Infectología e Inmunopatología, Unidad de Pediatría, Hospital Virgen del Rocío/Instituto de Biomedicina de Sevilla (IBiS), Seville, Spain;3. Non-Communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran;4. Department of Pediatric Pulmonary and Sleep Medicine, Children Medical Center, Tehran University of Medical Sciences, Tehran, Iran;5. Department of Immunology and Allergy, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran;6. Department of Allergy and Clinical Immunology, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, Iran;7. The Department of Immunology, Bahrami Hospital, Tehran University of Medical Sciences, Tehran, Iran;8. State Key Lab of Bioelectronics, School of Biological Science and Medical Engineering, Southeast University, Nanjing, China;9. Center for Research of Endemic Parasites of Iran, Tehran University of Medical Sciences, Tehran, Iran;10. Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Science, Tehran, Iran

Network for Immunology in Infection, Malignancy, and Autoimmunity (NIIMA), Universal Scientific Education and Research Network (USERN), Tehran, Iran;11. Research Center for Primary Immunodeficiencies, Iran University of Medical Sciences, Tehran, Iran

Division of Clinical Immunology, Department of Laboratory Medicine, Karolinska Institutet at the Karolinska University Hospital Huddinge, Stockholm, Sweden

Abstract:
Keywords:agammaglobulinemia  Bhalla scoring  high-resolution computed tomography  primary immunodeficiency  pulmonary function test  respiratory tract complications
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