Fetal case of congenital cystic adenomatoid malformation of the lung: fetal therapy and a review of the published reports in Japan |
| |
Authors: | Asabe Koushi Oka Yoichiro Shirakusa Takayuki |
| |
Institution: | Division of Pediatric Surgery, Maternity and Perinatal Care Center, Fukuoka University Hospital, 7-45-1 Nanakuma, Jonan-ku, Fukuoka, Japan. asabe@fukuoka-u.ac.jp |
| |
Abstract: | We herein report a case of type I congenital cystic adenomatoid malformation of the lung (CCAML) with non-immune hydrops fetalis (NIHF), a mediastinal shift and polyhydramnios diagnosed at 24 weeks' gestation by ultrasonography. The fetus was treated with a cyst-amniotic shunt at 29 weeks' gestation. Following a postnatal whole resection of the right lung, postpneumonectomy syndrome appeared and, as a result, the infant died 13 months after delivery due to respiratory failure. Only 19 cases demonstrating CCAML associated with NIHF have been reported previously in Japan. Four cases showed a spontaneous resolution of NIHF, while 5 cases with type I CCAML, which all underwent fetal intervention, demonstrated an excellent outcome. |
| |
Keywords: | congenital cystic adenomatoid malformation of the lung hydrops fetalis polyhydramnios |
本文献已被 PubMed 等数据库收录! |
|