Spiral Hypertrophic Cardiomyopathy as Detected by Cardiac Magnetic Resonance |
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| Authors: | Nessim Amin M.D. Ronald B. Williams B.A. June A. Yarmozik B.S. Robert W.W. Biederman M.D. F.A.C.C. F.A.H.A. |
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| Affiliation: | Department of Cardiac MRI, Allegheny General Hospital, , Pittsburgh, Pennsylvania |
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| Abstract: | Hypertrophic cardiomyopathy (HCM) is a genetically determined heart muscle disease; characterized by left ventricular hypertrophy. Spiral HCM is described as having a counterclockwise rotation pattern of hypertrophy along with variable degrees of fibrosis. A 34‐year‐old female presented with symptoms suggestive of heart failure. Echocardiography showed concentric left ventricular hypertrophy with normal contractility. Cardiac MRI showed asymmetric septal hypertrophy with mid‐cavity obliteration and a spiral pattern of variably increasing wall thickness. Late gadolinium enhancement demonstrated several areas of abnormal post‐gadolinium uptake. We report a case of spiral HCM. We should consider cardiovascular magnetic resonance as the reference standard for diagnosing HCM. |
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| Keywords: | cardiomyopathy hypertrophic cardiac magnetic resonance imaging |
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