| 噬血细胞综合征──附10例临床分析 |
| |
| 引用本文： | 肖燕,梁欣荃,费洪宝,金润铭,陈万新. 噬血细胞综合征──附10例临床分析[J]. 中国小儿血液与肿瘤杂志, 1999, 0(5) |
| |
| 作者姓名： | 肖燕 梁欣荃 费洪宝 金润铭 陈万新 |
| |
| 作者单位： | 同济医科大学附属协和医院儿科!４３００２２ |
| |
| 摘 要： | 噬血细胞综合征属于组织细胞增生性疾病，特征为组织细胞异常增生并具有吞噬血细胞现象。本文报道的１０例病列中，７例发现与感染相关，１例与肿瘤相关，２例未发现相关疾病。用大剂量丙种球蛋白治疗６例病人１例获得痊愈，３例临床症状好转，２例无效死亡。病例资料分析提示：血清甘油三脂增高和纤维蛋白原降低可能是预后不良的指标。
|
| 关 键 词： | 噬血细胞综合征 家族性噬血性淋巴组织细胞病 反应性噬血性组织 细胞病 |
HEMOPHAGOCYTIC SYNDRONE CIIINICAL ANALYSIS OF 10 CASES REPORTED |
| |
| Abstract: | Hemophagocytic syndrome (HPS) is one type of histiocytosis. It is characterized by exaggerated histiocytic proliferation and hemophagocytosis. There were 10 cases reported. 7 of10 cases was associated with infection, 1 cases was associated with malignancy, the associated disease has not been found in 2 cases. Among 6 cases who was treated with high-dose γ-globulin, 1 cases become recovery, clinical symptom become better in 3 cases, 2 cases whodid not respond to the treatment died. The clinical data suggested that hypertrigly ceridemiaand hypofibrinogenemia predict a bad prognosis. |
| |
| Keywords: | |
| 本文献已被 CNKI 等数据库收录！ |
|
