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Pulmonary Arterial Stent Implantation in an Adult with Williams Syndrome |
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| Authors: | Herre J. Reesink Onno D. F. Henneman Otto M. van Delden Jules D. Biervliet Jaap J. Kloek Jim A. Reekers Paul Bresser |
| Affiliation: | (1) Department of Pulmonology, Academic Medical Center, University of Amsterdam, F5-144, PO Box 22700, 1100, DE, Amsterdam, The Netherlands;(2) Department of Interventional Radiology, Academic Medical Center, University of Amsterdam, PO Box 22700, 1100, DE, Amsterdam, The Netherlands;(3) Department of Anesthesiology, Academic Medical Center, University of Amsterdam, PO Box 22700, 1100, DE, Amsterdam, The Netherlands;(4) Department of Cardiothoracic Surgery, Academic Medical Center, University of Amsterdam, PO Box 22700, 1100, DE, Amsterdam, The Netherlands |
| Abstract: | We report a 38-year-old patient who presented with pulmonary hypertension and right ventricular dysfunction due to pulmonary artery stenoses as a manifestation of Williams syndrome, mimicking chronic thromboembolic pulmonary hypertension. The patient was treated with balloon angioplasty and stent implantation. Short-term follow-up showed a good clinical result with excellent patency of the stents but early restenosis of the segments in which only balloon angioplasty was performed. These stenoses were subsequently also treated successfully by stent implantation. Stent patency was observed 3 years after the first procedure. |
| Keywords: | Balloon angioplasty Pulmonary artery stenosis Pulmonary hypertension Stent implantation Williams syndrome |
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