Pseudomixoma peritoneal tipo adenomucinosis peritoneal diseminada con imágenes radiológicas atípicas |
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Authors: | Manuel Vallalta Morales Ángel Segura Huerta Carmen Gil Adiego Laura Palomar Abad Jorge Molina Saera Roberto Díaz Beveridge |
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Affiliation: | 1. Servicio de Medicina Interna, Hospital Universitario La Fe, Valencia, Espa?a 2. Servicio de Oncología Médica, Hospital Universitario La Fe, Avenida Campanar 21, 46009, Valencia, Espa?a
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Abstract: | Pseudomyxoma peritonei is an unusual condition that has caused much confusion regarding its aetiology, clinical manifestations, treatment and prognosis. It is characterised by mucinous ascites and diffuse mucinous invasions of the peritoneum. Three histological subtypes have been defined: a) disseminated peritoneal adenomucinosis (peritoneal lesions composed of abundant extra-cellular mucin containing scant simple-to-focally-proliferating mucinous epithelium with little cytological atypia or mitotic activity); b) peritoneal mucinous carcinomatosis (peritoneal lesions composed of more abundant mucinous epithelium with the architectural and cytological features of carcinoma); and c) an intermediate group. The different histological subtypes have different prognoses. We report a case of disseminated peritoneal adenomatosis, and discuss its clinical management. |
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