原发性肺动脉肉瘤的诊治进展

原发性肺动脉肉瘤是一种起源于肺动脉并主要累及肺循环的罕见肿瘤,其临床表现多样且无特异性,易复发和转移.本病与慢性肺血栓栓塞疾病在临床和影像学表现方面存在相似性而容易混淆,不同影像学诊断方法联合有助于提高术前诊断率.治疗以手术为主,联合化疗和放疗可延长生存期.本病总体预后差,与肿瘤切除程度、病理类型等相关.

Advancement in diagnosis and treatment of primary pulmonary artery sarcoma

Primary pulmonary artery sarcoma is a rare tumor that originates from pulmonary artery and mainly affects pulmonary circulation.The clinical manifestations of primary pulmonary artery sarcoma are multiplex and nonspecific,and the disease is prone to relapse and metastasis.This disease is often confused with chronic pulmonary thromboembolism,as both have similar clinical and imaging manifestations.The combination of different imaging methods can elevate the preoperative diagnosis rate.Surgery is the primary treatment,however the combination with chemotherapy and radiotherapy can prolong life span.The prognosis of the disease is poor and associated with surgery mode and histology.