漏斗胸合并肺部疾病的诊断和治疗

目的 回顾先天性漏斗胸合并肺部疾病的病例,探讨诊断方法及治疗原则.方法 2002年7月至2011年8月回顾性分析91例合并肺部疾病漏斗胸患儿的临床资料.其中男64例,女27例.术前常规行胸部X线平片和CT检查,其中影像学证实的漏斗胸同时合并先天性肺囊肿、先天性肺囊性腺瘤样畸形、肺隔离症、肺大疱及部分较严重的肺气肿患儿30例,均同期行漏斗胸Nuss手术和开胸肺叶切除手术.结果 30例病例均顺利完成同期漏斗胸Nuss手术及肺叶切除手术,且最终均通过病理诊断证实.术后随访效果良好.结论 胸部CT扫描检查是诊断先天性漏斗胸合并肺部疾病的有效方法.微创Nuss手术给同期行肺叶切除手术带来了可能.同期手术减少了患儿多次手术的手术风险,同时减轻了患者家属的经济负担.

The diagnosis and treatment of pectus excavatum associated with congenital pulmonary disease in children

Objective To summarize the experience of diagnosis and treatment of pectus excavatum associated with congenital pulmonary disease in children.Methods The data of 91 patients with pectus excavatum associated with congenital pulmonary disease was collected from July 2002 to August 2010 in Beijing Children's Hospital.There were 64 males and 27 females.30 patients with pectus excavatum associated with congenital pulmonary cyst,congenital cystic adenomatoid malformation,pulmonary sequestration,and some severe cases of congenital lobar emphysema received the Nuss surgery and lobectomy simultaneously.Results 30 cases with pectus excavatum asseeiated with congenital pulmonary disease received simultaneous Nuss procedure and lobectomy.All cases were confirmed by pathology and recovered uneventfully.Conclusion Chest CT scan is an effective way to evaluate pectus excavatum associated with pulmonary diseases.Whether surgery is needed for the pulmonary disease depend on the specific types of disease,age and other various factors.Simultaneous surgery for pectus excavatum and pulmonary disease can lower the risk of the multiple operations,and reduce the financial burden of famihes.