儿童门静脉海绵样变间接门静脉造影特点

目的探讨儿童门静脉海绵样变(CTPV)的间接门脉造影表现及其临床意义。方法回顾性分析了8例经超声诊断及造影证实的门静脉海绵样变患儿的间接门脉造影血管造影图像,观察其特征性的血管造影表现,并对其指导临床治疗的意义进行了评价。结果8例中6例清楚显示门脉主要分支近肝门处阻塞,2例门静脉主干阻塞,代之以肿块样纡曲血管并在其周围形成向肝内放射状的侧支血管影像,以及离肝性侧支循环静脉。8例血管造影均能对与分流或断流手术有关的血管解剖提供准确信息。结论儿童CTPV具有特征性的血管造影表现,间接门脉造影对CTPV的诊断和治疗有重要价值。

Children''s cavernous transformation of the portal vein: the arterial portographic features

Objective To study the arterial portographic features of children's cavernous transformation of the portal vein(CTPV).Methods Angiographic findings of the arterial portography of 8 children with CTPV were retrospectively analyzed.Results Occlusion of the main branch of portal vein at the porta hepatis was revealed in 6 out of 8 cases, and a masslike network of tortuose veins around the porta hepatis and many small irregular veins radiating from the network to the liver were demonstrated.Both hepatopetal and reverse flow of collateral venous pathways were found.Conclusion Children's CTPV have very characteristic angiographic findings,which can be very helpful for surgical management.