Agminated Fibroblastic Conective Tissue Nevus: A New Clinical Presentation |
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| Authors: | Camila Downey MD Luis Requena MD Silvia Bagué MD Miquel Ángel Sánchez Martínez MD Josep Lloreta MD Eulalia Baselga MD PhD |
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| Institution: | 1. Department of Dermatology, Facultad de Medicina, Pontificia Universidad Católica de Chile, Santiago, Chile;2. Department of Dermatology, Fundación Jiménez Díaz, Madrid, Spain;3. Department of Pathology, Hospital de la Santa Creu I Sant Pau, Barcelona, Spain;4. Department of Dermatology, Hospital de la Santa Creu I Sant Pau, Barcelona, Spain;5. Department of Pathology, Hospital del Mar, Barcelona, Spain |
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| Abstract: | Connective tissue nevi are benign hamartomatous lesions in which one or several of the components of the dermis (collagen, elastin, glicosaminoglycans) show predominance or depletion. Recently, de Feraudy et al broadened the spectrum of connective tissue nevus, describing fibroblastic connective tissue nevus (FCTN), which is characterized by proliferation of CD34+ cells of fibroblastic and myofibroblastic lineage. Only solitary papules and nodules have been described. We present the first case of FCTN with multiple agminated lesions on the leg of an infant and the difficulties encountered in the differential diagnosis with dermatofibrosarcoma protuberans. |
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