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Congenital Fatal Diarrhea in Newborns
Authors:Swapna Lingaldinna  Mangala Bharathi Sundaram  C N Kamalarathnam  Sumathi Bavanandam
Institution:1.Department of Neonatology,Institute of Child Health and Hospital for Children,Chennai-8,India;2.Department of Pediatric Gastroenterology,Institute of Child Health and Hospital for Children,Chennai-8,India
Abstract:Microvillus inclusion disease is a rare autosomal recessive disorder of intestinal epithelium causing intractable secretary diarrhea in the first two months of life and about 140 cases have been reported worldwide till now. Here authors report 2 cases of Microvillus inclusion disease (MVID) diagnosed in neonates by electron microscopy study of small intestinal biopsy.
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