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遗传性运动感觉性神经病合并肥厚性心肌病的PDE、3D-TCD、EEG、BAEP和ECG的对比分析
引用本文:崔毅,王舒亚,张志锁,刘莹. 遗传性运动感觉性神经病合并肥厚性心肌病的PDE、3D-TCD、EEG、BAEP和ECG的对比分析[J]. 现代电生理学杂志, 1997, 0(3)
作者姓名:崔毅  王舒亚  张志锁  刘莹
作者单位:上海第二军医大学长海医院(崔毅,王舒亚,张志锁),上海第二军医大学长海医院(刘莹)
摘    要:本文报告1家3代遗传性运动感觉性神经病(HMSN)合并肥厚性心肌病(HCM)12例患者及1例无症状者的多普勒超声心动图(PDE),三维彩色经颅多普勒(3D—TCD),脑电图(EEG),脑干听觉诱发电位(BAEP)和心电图(ECG)。结果表明:PDE、3DTCD、EEG、BAEP和ECG异常率分别是85.6%,84.6%,76.9%,92.3%和92.3%。

关 键 词:遗传性运动感觉性神经病  脑干听觉诱发电位

COMPARATIVE ANALYSES OF PDE,3D-TCD.EEG,BAEP AND ECG IN PATIENTS WITH HMSN AM) HCM
Chui Yi Wang Shuya Zhang Zhisuo,et al Changhai Hospital,Shanghai.. COMPARATIVE ANALYSES OF PDE,3D-TCD.EEG,BAEP AND ECG IN PATIENTS WITH HMSN AM) HCM[J]. Journal of Modern Electrophysiology, 1997, 0(3)
Authors:Chui Yi Wang Shuya Zhang Zhisuo  et al Changhai Hospital  Shanghai.
Affiliation:Chui Yi Wang Shuya Zhang Zhisuo,et al Changhai Hospital,Shanghai. 200433
Abstract:PDE,3D-TCD,EEG,BAEP and EGG were examined in 13 patients withHMSN and HCM.The results showed that their abnormal rates were 85.6%.84.6%.76.9%,92.3 and 92.3%rcspeetivcly.
Keywords:hereditary motor-sensory neuropathy  brain stem auditory evoked potential
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