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Type 1 Autoimmune Pancreatitis Extending along the Main Pancreatic Duct: IgG4-related Pancreatic Periductitis
Authors:Junya Sato  Hiroyuki Matsubayashi  Hirotoshi Ishiwatari  Tatsunori Satoh  Junichi Kaneko  Kazuma Ishikawa  Masao Yoshida  Kohei Takizawa  Yohei Yabuuchi  Yoshihiro Kishida  Kenichiro Imai  Kinichi Hotta  Katsuhiko Uesaka  Keiko Sasaki  Hiroyuki Ono
Affiliation:1.Division of Endoscopy, Shizuoka Cancer Center, Japan; 2.Division of Genetic Medicine Promotion, Shizuoka Cancer Center, Japan; 3.Division of Hepato-Biliary-Pancreatic Surgery, Shizuoka Cancer Center, Japan; 4.Division of Pathology, Shizuoka Cancer Center, Japan
Abstract:We herein report a unique form of autoimmune pancreatitis (AIP) spreading along the main pancreatic duct (MPD). A 70-year-old man was referred for a small lesion at the pancreatic neck, accompanying an adjacent cyst and dilated upstream MPD. Four years earlier, health checkup images had shown a pancreatic cyst but no mass lesion. Endoscopic ultrasonography showed a contrast-enhanced, tumorous lesion, mainly occupying the MPD. With a preoperative diagnosis of ductal neoplasms mainly spreading in the MPD, Whipple''s resection was performed. The resected specimens showed MPD periductitis with IgG4-related pathology, indicating type 1 AIP. Clinicians should practice caution concerning the various AIP forms.
Keywords:autoimmune pancreatitis   IgG4   periductitis   intraductal neoplasms   diagnosis
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